Cystic fibrosis therapies

Christabella Ng; Alan R. Smyth

doi:10.1016/B978-0-08-102723-3.00106-2

Cystic fibrosis therapies

Research output: Chapter in Book/Report/Conference proceeding › Chapter

Abstract

Cystic fibrosis (CF) is a multi-system genetic disorder. Therapies are primarily focused on preserving lung function and nutrition from childhood through to adulthood. Early detection and effective clinical management of CF is key to limiting disease progression (Bell et al., 2020; Sermet-Gaudelus et al., 2011). Chronic illnesses carry high treatment burden and therefore it is essential that treatments are rationalized where possible. This article will outline the therapies used to prevent CF disease progression and therapies used for disease complications. The use of therapies for the basic defect of CF will be discussed in another chapter.

Original language	English
Title of host publication	Encyclopedia of respiratory medicine
Editors	Sam M Janes
Publisher	Elsevier Inc.
Pages	179-187
Number of pages	9
Volume	6
Edition	2
ISBN (Electronic)	9780081027240
ISBN (Print)	9780081027233
DOIs	https://doi.org/10.1016/B978-0-08-102723-3.00106-2
Publication status	Published - 01 Jan 2021
Externally published	Yes

Bibliographical note

Publisher Copyright:
© 2022 Elsevier Ltd. All rights reserved

Keywords

Airway clearance techniques
Allergic bronchopulmonary aspergillus
Anti-pseudomonas treatment
Antibiotics
Cystic fibrosis (CF)
Cystic fibrosis related bone disease
Cystic fibrosis related diabetes
Cystic fibrosis related liver disease
Distal intestinal obstruction syndrome
Non-tuberculous mycobacteria treatment
Prophylactic antibiotics
Therapies

ASJC Scopus subject areas

General Medicine

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

Access to Document

10.1016/B978-0-08-102723-3.00106-2Licence: Unspecified

Cite this

@inbook{69e2eb1de70c45de888b4d54ee75d53d,

title = "Cystic fibrosis therapies",

abstract = "Cystic fibrosis (CF) is a multi-system genetic disorder. Therapies are primarily focused on preserving lung function and nutrition from childhood through to adulthood. Early detection and effective clinical management of CF is key to limiting disease progression (Bell et al., 2020; Sermet-Gaudelus et al., 2011). Chronic illnesses carry high treatment burden and therefore it is essential that treatments are rationalized where possible. This article will outline the therapies used to prevent CF disease progression and therapies used for disease complications. The use of therapies for the basic defect of CF will be discussed in another chapter.",

keywords = "Airway clearance techniques, Allergic bronchopulmonary aspergillus, Anti-pseudomonas treatment, Antibiotics, Cystic fibrosis (CF), Cystic fibrosis related bone disease, Cystic fibrosis related diabetes, Cystic fibrosis related liver disease, Distal intestinal obstruction syndrome, Non-tuberculous mycobacteria treatment, Prophylactic antibiotics, Therapies",

author = "Christabella Ng and Smyth, {Alan R.}",

year = "2021",

month = jan,

day = "1",

doi = "10.1016/B978-0-08-102723-3.00106-2",

language = "English",

isbn = "9780081027233",

volume = "6",

pages = "179--187",

editor = "Janes, {Sam M }",

booktitle = "Encyclopedia of respiratory medicine",

publisher = "Elsevier Inc.",

address = "United States",

edition = "2",

}

TY - CHAP

T1 - Cystic fibrosis therapies

AU - Ng, Christabella

AU - Smyth, Alan R.

PY - 2021/1/1

Y1 - 2021/1/1

N2 - Cystic fibrosis (CF) is a multi-system genetic disorder. Therapies are primarily focused on preserving lung function and nutrition from childhood through to adulthood. Early detection and effective clinical management of CF is key to limiting disease progression (Bell et al., 2020; Sermet-Gaudelus et al., 2011). Chronic illnesses carry high treatment burden and therefore it is essential that treatments are rationalized where possible. This article will outline the therapies used to prevent CF disease progression and therapies used for disease complications. The use of therapies for the basic defect of CF will be discussed in another chapter.

AB - Cystic fibrosis (CF) is a multi-system genetic disorder. Therapies are primarily focused on preserving lung function and nutrition from childhood through to adulthood. Early detection and effective clinical management of CF is key to limiting disease progression (Bell et al., 2020; Sermet-Gaudelus et al., 2011). Chronic illnesses carry high treatment burden and therefore it is essential that treatments are rationalized where possible. This article will outline the therapies used to prevent CF disease progression and therapies used for disease complications. The use of therapies for the basic defect of CF will be discussed in another chapter.

KW - Airway clearance techniques

KW - Allergic bronchopulmonary aspergillus

KW - Anti-pseudomonas treatment

KW - Antibiotics

KW - Cystic fibrosis (CF)

KW - Cystic fibrosis related bone disease

KW - Cystic fibrosis related diabetes

KW - Cystic fibrosis related liver disease

KW - Distal intestinal obstruction syndrome

KW - Non-tuberculous mycobacteria treatment

KW - Prophylactic antibiotics

KW - Therapies

U2 - 10.1016/B978-0-08-102723-3.00106-2

DO - 10.1016/B978-0-08-102723-3.00106-2

M3 - Chapter

AN - SCOPUS:85143106582

SN - 9780081027233

VL - 6

SP - 179

EP - 187

BT - Encyclopedia of respiratory medicine

A2 - Janes, Sam M

PB - Elsevier Inc.

ER -

Cystic fibrosis therapies

Abstract

Bibliographical note

Keywords

ASJC Scopus subject areas

UN SDGs

Access to Document

Fingerprint

Cite this