Temper outbursts in Prader-Willi syndrome: causes, behavioural and emotional sequence and responses by carers

P. Tunnicliffe*, K. Woodcock, L. Bull, C. Oliver, J. Penhallow

*Corresponding author for this work

Research output: Contribution to journalArticle

25 Citations (Scopus)

Abstract

Background: Temper outbursts are common in Prader-Willi syndrome but rarely described in detail. This study investigated the phenomenology of temper outbursts in terms of antecedents, sequence of behaviours and emotions and intervention strategies used.

Method: A semi-structured interview about temper outbursts was conducted with the main carers of seven children (9.5 to 16.7 years) and seven adults (24.7 to 47.10 years) with Prader-Willi syndrome (10 male, 4 female). Reliability and validity of the interview results was established.

Results: Various setting events increased and reduced the likelihood of temper outbursts. The most common antecedent was a change to routine or expectation. There were marked similarities in the sequence of behaviours and emotions during temper outbursts, with anger rising quickly followed by expressions of remorse and distress at the end of an outburst.

Discussion: The sequence of behaviours and emotions within outbursts was similar to that described in temper tantrums in typical development. Cognitive and emotional processes are likely to be important in the understanding of temper outbursts with implications for early intervention.

Original languageEnglish
Pages (from-to)134-150
Number of pages17
JournalJournal of Intellectual Disability Research
Volume58
Issue number2
DOIs
Publication statusPublished - Feb 2014

Keywords

  • behavioural phenotypes
  • challenging behaviour
  • intellectual disability
  • Prader-Willi syndrome
  • temper outbursts
  • SELF-INJURIOUS-BEHAVIOR
  • SMITH-MAGENIS-SYNDROME
  • ESTABLISHING OPERATIONS
  • MALADAPTIVE BEHAVIOR
  • YOUNG-CHILDREN
  • INTELLECTUAL DISABILITY
  • CHALLENGING BEHAVIOR
  • POPULATION
  • TANTRUMS
  • PREVALENCE

ASJC Scopus subject areas

  • Clinical Neurology
  • Neurology
  • Psychiatry and Mental health
  • Rehabilitation
  • Arts and Humanities (miscellaneous)

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